Molecular structure pattern

Pulmonary Arterial Hypertension References

Last updated: 09 September 2026
  1. Medworm - Pulmonary Hypertensionhttp://www.medworm.com/rss/medicalfeeds/conditions/Pulmonary-Hypertension.xml
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  13. Sitbon O, Cottin V, Canuet M, et al. Initial combination therapy of macitentan and tadalafil in pulmonary arterial hypertension. Eur Respir J. 2020 Sep;56(3):2000673. doi: 10.1183/13993003.00673-2020. Accessed 22 Oct 2020. PMID: 32350101
  14. Thomas CA, Anderson RJ, Condon DF, et al. Diagnosis and management of pulmonary hypertension in the modern era: insights from the 6th world symposium. Pulm Ther. 2020 Jun;6(1):9-22. doi: 10.1007/s41030-019-00105-5. Accessed 19 Oct 2020. PMID: 32048239
  15. Eichstaedt CA, Belge C, Chung WK, et al. Genetic counselling and testing in pulmonary arterial hypertension: a consensus statement on behalf of the International Consortium for Genetic Studies in PAH. Eur Respir J. 2023 Feb;61(2):2201471. doi: 10.1183/13993003.01471-2022. PMID: 36302552
  16. Humbert M, Kovacs G, Hoeper MM, et al. 2022 ESC/ERS guidelines for the diagnosis and treatment of pulmonary hypertension. Eur Heart J. 2022 Oct;43(38):3618-3731. doi: 10.1093/eurheartj/ehac237. PMID: 36017548
  17. Maron BA. Revised definition of pulmonary hypertension and approach to management: a clinical primer. J Am Heart Assoc. 2023 Apr;12(8):e029024. doi: 10.1161/JAHA.122.029024. PMID: 37026538
  18. Torbic H, Tonelli AR. Sotatercept for pulmonary arterial hypertension in the inpatient setting. J Cardiovasc Pharmacol Ther. 2024 Jan-Dec;29:10742484231225310. doi: 10.1177/10742484231225310. PMID: 38361351
  19. GBD 2021 Stroke Risk Factor Collaborators. Global, regional, and national burden of stroke and its risk factors, 1990-2021: a systematic analysis for the Global Burden of Disease Study 2021. Lancet Neurol. 2024;23(10):973-1003. doi: 10.1016/S1474-4422(24)00369-7. Accessed 07 Jun 2025. PMID: 39304265
  20. Huang S, Qiu J, Wang A, et al. Burden of pulmonary arterial hypertension in Asia from 1990 to 2021: findings from Global Burden of Disease Study 2021. Chin Med J (Engl). 2025 Jun;138(11). doi: 10.1097/CM9.0000000000003559. Accessed 07 Jun 2025. PMID: 40375470
  21. Hopkins W, Rubin LJ. Treatment and prognosis of pulmonary arterial hypertension in adults (group 1). UpToDate. https://www.uptodate.com. 18 Dec 2025.
  22. Kovacs G, Bartolome S, Denton CP, et al. Definition, classification and diagnosis of pulmonary hypertension. Eur Respir J. 2024 Oct;64(4):2401324. doi: 10.1183/13993003.01324-2024. Accessed 24 Feb 2026. PMID: 39209475
  23. Rubin LJ, Hopkins W. The epidemiology and pathogenesis of pulmonary arterial hypertension (group 1). UpToDate. https://www.uptodate.com. 03 Feb 2026.
  24. Belkin MN, Fudim M, Baratto C, et al. Standardization of baseline and provocative invasive hemodynamic protocols for the evaluation of heart failure and pulmonary hypertension: a scientific statement from the American Heart Association. Circ Heart Fail. 2026 Feb;19(2):e000088. PMID: 41493051
  25. DuBrock HM, Savale L, Sitbon O, et al. International Liver Transplantation Society practice guideline update on portopulmonary hypertension. Liver Transpl. 2026 Feb;32(2):296-314. doi: 10.1097/LVT.0000000000000600. Accessed 31 Aug 2026. PMID: 40094355
  26. Hopkins W, Rubin LJ, Chin K, et al. Treatment of pulmonary arterial hypertension (group 1) in adults: pulmonary hypertension-specific therapy. UpToDate. https://www.uptodate.com. 03 Aug 2026. Accessed 31 Aug 2026.
  27. Sahay S, Visovatti S, Tonelli AR, et al. International Society for Heart and Lung Transplantation (ISHLT) consensus statement on risk stratification in pulmonary arterial hypertension. J Heart Lung Transplant. 2025 Nov;44(11):e73-e131. doi: 10.1016/j.healun.2025.04.015. PMID: 40910964